From Dog
Anotia in a St. Bernard pup. The arrow indicates the anotia and auricular scar[1]

Anotia, an autosomal-recessive congenital disease of dogs, is defined as a congenital absence of either one or both ears (pinna).

In dogs, this has been reported in the St. Bernard associated with hereditary polydactyly[1], oral deformities such as bifid tongue and cleft palate as well as extra thoracic vertebrae and ribs.

The cause of this condition is unknown.

Affected dogs have normal hearing despite pups having no or only a vestigial auricular tag and atresic auditory canals. The inner ear appears normal, including the tympanic membrane and the auditory ossicles.


  1. 1.0 1.1 Villagómez DA & Alonso RA (1998) A distinct Mendelian autosomal recessive syndrome involving the association of anotia, palate agenesis, bifid tongue, and polydactyly in the dog. Can Vet J 39(10):642-643